Desmoid tumors beiong to a group of disorders called fibromatoses, which are charecterized by fibroblastic proliferation without evidence of inflammation or definite neoplasia. Historically, the desmoid fibromatoses have been divided into those
affecting the soft tissue, usually striated muscle, of abdominal wall(the abdominal desmoid) and those affecting other region (the extraabdominal desmoid), also known as musculoaponeurotic fibromatoses. Desmoid may occur at any age, with a peak
incidence in the 3rd decade. Extraabdominal desmoids usally occur in the soft tissue of extremities, pelvis, buttock and neck. It is unusual in chest wall. Authors experienced a case of desmoid tumor of the chest wall. CT scan showed poorly
marginated
soft tissue mass under pectoralis musclo, involving 1st chondrosternal junction, with slight and inhomogeneous contrast enhancment. RI bone scan was normal. Enblock resection was done, and confirmed fibroblastic overgrowth.
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